PRNP
PRNP,即朊蛋白前體,別名AltPrP、ASCR、CD230。它是一種由PRNP基因編碼的蛋白質(zhì),廣泛存在于人體多種組織中,尤其在中樞神經(jīng)系統(tǒng)。PRNP的作用機(jī)制涉及其正常形式PrPC參與細(xì)胞黏附和信號(hào)傳導(dǎo),而當(dāng)PrPC錯(cuò)誤折疊成PrPSc時(shí),會(huì)形成淀粉樣纖維并積累,引發(fā)神經(jīng)細(xì)胞損傷。PRNP的生物學(xué)意義在于其與多種神經(jīng)退行性疾病密切相關(guān),尤其是朊病毒病,如克雅氏病等,這些疾病由PrPSc的異常聚集導(dǎo)致,目前尚缺乏有效治療手段,使PRNP成為神經(jīng)科學(xué)研究的重要靶點(diǎn)。
熱銷產(chǎn)品
PRNP Antibody (CSB-PA018739LA01HU)
驗(yàn)證數(shù)據(jù)

Immunohistochemistry of paraffin-embedded human pancreatic cancer using CSB-PA018739LA01HU at dilution of 1:100

Immunofluorescent analysis of PC-3 cells using CSB-PA018739LA01HU at dilution of 1:100 and Alexa Fluor 488-congugated AffiniPure Goat Anti-Rabbit IgG(H+L)
Human Major prion protein(PRNP) ELISA kit (CSB-EL018739HU)
驗(yàn)證數(shù)據(jù)

貨號(hào):CSB-EL018739HU
規(guī)格:96T/48T
靈敏度:0.078 ng/mL
檢測(cè)范圍:0.312 ng/mL-20 ng/mL
These standard curves are provided for demonstration only. A standard curve should be generated for each set of samples assayed.
PRNP Antibodies
PRNP for Homo sapiens (Human)
產(chǎn)品貨號(hào) | 產(chǎn)品名稱 | 種屬反應(yīng)性 | 應(yīng)用類型 |
---|---|---|---|
CSB-PA018739GA01HU | PRNP Antibody | Human,Mouse,Rat | ELISA,WB,IHC |
CSB-PA018739LA01HU | PRNP Antibody | Human | ELISA, IHC, IF |
CSB-PA018739LB01HU | PRNP Antibody, HRP conjugated | Human | ELISA |
CSB-PA018739LC01HU | PRNP Antibody, FITC conjugated | Human | |
CSB-PA018739LD01HU | PRNP Antibody, Biotin conjugated | Human | ELISA |
PRNP ELISA Kit
PRNP ELISA Kit for Homo sapiens (Human)
產(chǎn)品貨號(hào) | 產(chǎn)品名稱 | 樣本類型 | 靈敏度 |
---|---|---|---|
CSB-EL018739HU | Human Major prion protein(PRNP) ELISA kit | serum, plasma, tissue homogenates | 0.078 ng/mL |